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59

SBA. Neonatal pulse oximetry screening

60

SBA. McCune Albright syndrome

61

MCQ. The Kleihauer test

62

EMQ. Listeriosis and pregnancy

63

MCQ. Folic acid fortification of flour

64

EMQ. Mental Capacity Act

65

EMQ. Cri du chat syndrome

66

EMQ. Anatomy of the fetal skull

67

EMQ. Flu and pregnancy

 

59.   Neonatal pulse oximetry screening.

Abbreviations.

cCHD:            critical congenital heart disease.

CHD:             congenital heart disease.

NPOS:           neonatal pulse oximetry screening.

NSC:              National Screening Committee.

RDS:              respiratory distress syndrome, AKA SDLDN.

Question 1.   Which of the following best describes the purpose of NPOS?

A

detection of congenital heart disease

B

detection of critical congenital heart disease

C

detection of uncritical congenital heart disease

F

detection of hypoplastic left heart

E

detection of patent ductus arteriosus

D

differentiating between transient tachypnoea of the newborn and RDS

G

none of the above

Question 2.   What is the approximate incidence of CHD in neonates?

A

1 in 50

B

1 in 100

C

1 in 150

D

1 in 200

E

1 in 250

F

1 in 300

G

none of the above

Question 3.   What is the approximate % of CHD that is critical CHD in neonates?

A

10%

B

15%

C

20%

D

25%

E

30%

F

35%

G

40%

Question 4.   What is the National Screening Committee’s advice on NPOS?

A

all NHS units to have it established by March 2026

B

all NHS units to have it established by March 2030

C

further research needed into cost-benefit ratio

D

further research needed into adverse outcomes after false +ve results

E

further research needed into risks of “overdiagnosis”

F

further research needed into risk/benefit for non-cardiac conditions

G

none of the above

Question 5.   What is the sensitivity of NPOS for detecting cCHD before discharge from hospital?

A

~ 50%

B

~60 %

C

~ 70%

D

~ 80%

E

~ 90%

F

~100 %

Question 6.   What % of NHS Trusts have introduced NPOS despite the NSC’s reservations?

A

~ 50%

B

~60 %

C

~ 70%

D

~ 80%

E

~ 90%

F

~100 %

 

60.   McCune Albright syndrome.

Abbreviations.

CPP:      central precocious puberty.

MCA:    McCune Albright syndrome.

PFD:      polyostotic fibrous dysplasia.

PP:         precocious puberty.

Scenario 1.    Which, if any, of the following are components of the classical triad of MCA?

A

albinism

B

“cafè Cubano” spots

C

“Coast of California” pigmented areas

D

lentigo

E

macroorchidism

F

osteomalacia

G

polyostotic fibrous dysplasia

H

precocious puberty

I

premature menopause

J

primary amenorrhoea

Scenario 2.    Which, if any, of the following are true in relation to MCA?

A

it is an example of central primary amenorrhoea

B

it is an example of central secondary amenorrhoea

C

it is an example of central precocious puberty

D

it is an example of peripheral primary amenorrhoea

E

it is an example of peripheral secondary amenorrhoea

F

it is an example of peripheral precocious puberty

G

none of the above

Scenario 3.    Which, if any, of the following are believed to be true in relation to the abnormality of

onset of puberty associated with MCA?

A

it is due to abnormal FSH production

B

it is due to abnormal LH production

C

it may be due to abnormal androgen production

D

it may be due to abnormal oestrogen production

E

it is linked to ovarian cysts with ↑ malignant potential

F

none of the above

Scenario 4.    Which, if any, of the following are true in relation to polyostotic fibrous dysplasia?

A

polyostotic means resembling parrot bone

B

polyostotic means resembling pigeon bone

C

polyostotic means affecting long bones

D

fibrous dysplasia refers to replacement of marrow by fibrous tissue

E

PFD is a variant of osteomalacia

F

PFD may be unilateral

G

PFD is associated with a 1% risk of malignancy

Scenario 5.    Which, if any, of the following are true in relation to MCA?

A

hyperthyroidism is common

B

hypothyroidism is common

C

thyroid function is similar to those without MCA

Scenario 6.    Which, if any, of the following are true in relation to MCA?

A

excess growth hormone production  is common

B

inadequate growth hormone production is common

C

growth hormone production is similar to those without MCA

Scenario 7.    Which, if any, of the following is true in relation to MCA?

A

inheritance is autosomal dominant

B

inheritance is autosomal recessive

C

inheritance is X-linked dominant

D

inheritance is X-linked recessive

E

inheritance is multifactorial

F

it is not a hereditary disorder

G

it is not genetic

H

none of the above

Scenario 8.    Which, if any, of the following are true in relation to MCA?

A

renal artery stenosis is more common

B

renal cortex wasting is more common

C

renal phosphate wasting is more common

D

renal waisting is more common

E

none of the above.

Scenario 9.    Approximately what % of children born to women with MCAS will have MCAS?

A

0

B

1 in 105 - 106

C

1 in 104

D

1 in 100

E

1 in 50

F

1 in 10

G

1 in 2

H

All

TOG includes MCAS in CPD Questions for volume 14, number 2, 2012, which are open access, so reproduced here. There are only two questions on MCAS. Note that the second includes CPP.

McCune–Albright syndrome

1. is caused by activating mutations of the GNAS1 gene.                                            True / False

2. is characterised by polyostotic fibrous dysplasia, café-au-lait spots and CPP.      True / False

 

61.   The Kleihauer test.

Answer True / False

a.  may be used to confirm the presence of Rhesus antibodies.

b.  should be performed routinely at 28 and 36 weeks in the woman who is Rhesus negative.

c.   'ghost' cells may be seen, indicating that the patient is a follower of Dracula and "undead".

d.  is no longer required after delivery in the Rhesus negative woman.

e.  is based on the relative resistance of fetal haemoglobin to denaturation using ultra-violet light.

f.   only gives +ve results in women who are Rhesus +ve.

g.  should be done as part of the investigation of fetal death in utero for all women, regardless of their blood group and that of their babies.

 

62.   Listeriosis and pregnancy.

Abbreviations.

Lm:     Listeria monocytogenes.

TOC:   test of cure.

Scenario 1.         Which organism is responsible for human listeriosis?

A

Listeria diogenys

B

Listeria frigidaire

C

Listeria hominis

D

Listeria monocytogenes

E

Listeria xenophylus

Scenario 2.         Which, if any, of the following statements are true about Lm?

Option list.

A

it is a small, Gram -ve rod

B

it is a Gram +ve coccus

C

it is flagellated

D

it has no cell wall

E

it is an obligate aerobe

F

it functions within host cells

G

it can easily be mistaken for commensal organisms

H

none of the above

Scenario 3.         Which of the following are associated with an increased risk of contracting LM?

A

age > 60 years

B

age < 1 year

C

blond hair

D

pregnancy

E

strabismus

Scenario 4.         Which of the following are true of the susceptibility of pregnant women to Lm?

Option list.

A

they are not more susceptible

B

they are more susceptible x 2

C

they are more susceptible x 5

D

they are more susceptible x 10

E

they are more susceptible x 20

F

they are > 20 times more susceptible

G

none of the above.

Scenario 5.         When does Lm most often occur?

Option list.

A

1st. trimester

B

2nd. trimester

C

3rd trimester

D

1st. + 2nd. trimesters

E

2nd. + 3rd trimesters

F

all trimesters equally

G

puerperium

H

none of the above

Scenario 6.         What is the incubation period for Lm?.

Option list.

A

7±3 days

B

7±5 days

C

10±3 days

D

10±5 days

E

14±3 days

F

14±5 days

G

none of the above.

Scenario 7.         What is the significance of Granulomatosis Infantisepticum ?

Option list.

A

it is a fabrication by the author and of no significance

B

it is pathognomonic of Lm infection

C

it is the cause of vertical transmission of Lm

D

I refuse to answer Latin questions as they make me think of Boris Johnson

E

none of the above

Scenario 8.         Which of the following are accurate about cervico-vaginal infection? This is not a true

EMQ as there may be >1 correct answer.

Option list.

A

Lm is as often found in the cervix as in the bowel.

B

Lm is as often found in the vagina as in the bowel.

C

Lm is less often  found in the cervix than in the bowel.

D

Lm is less often  found in the vagina than in the bowel.

E

Lm is more often  found in the cervix than in the bowel.

F

Lm is more often  found in the cervix than in the bowel.

G

no one knows and no one cares

Scenario 9.         A GP phones about a primigravida at 28 weeks. She has possibly ingested food

contaminated by Lm. She is asymptomatic and afebrile. What advice will you give?

Option list.

A

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 2 weeks

B

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 4 weeks

C

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 6 weeks

D

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 8 weeks

E

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

F

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

G

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

H

admit to hospital for investigation and intensive treatment if Lm infection found

I

none of the above

Scenario 10.      A GP phones about a primigravida at 28 weeks. She has possibly ingested food

contaminated by Lm. She has mild symptoms but is afebrile. What advice will you give?

Option list.

A

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 2 weeks

B

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 4 weeks

C

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 6 weeks

D

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 8 weeks

E

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

F

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

G

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

H

admit to hospital for investigation and intensive treatment if Lm infection found

I

none of the above

Scenario 11.      A GP phones about a primigravida at 28 weeks. She has possibly ingested food

contaminated by Lm. She is symptomatic and her temperature is 38.2oC. What advice will you give?

Option list.

A

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 2 weeks

B

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 4 weeks

C

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 6 weeks

D

reassure and advise her about avoiding exposure and to reattend if she develops signs or symptoms within 8 weeks

E

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

F

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

G

prescribe appropriate antibiotic(s) for 7 days with follow-up for TOC

H

admit to hospital for investigation and intensive treatment if Lm infection found

I

none of the above

Scenario 12.      Which, if any, of the following would be appropriate for consideration as 1st. line

treatment of Lm in pregnancy? This is not a true EMQ as there may be more than 1 correct answer.

Option list.

A

ampicillin

B

ampicillin + gentamycin

C

ampicillin + streptomycin

D

amoxicillin + clavulanic acid

E

clarithromycin

F

erythromycin

G

erythromycin + metronidazole

H

trimethoprim

I

none of the above

Scenario 13.      Is listeriosis a notifiable infection in the UK? Yes/No.

 

63.   Folic acid fortification of flour.

Abbreviations.

FFF:                  fortification of flour with folic acid.

NTD:                 neural tube defect.

Scenario 1.         What is the incidence of NTD in the UK?

Scenario 2.         What is the risk of an affected sibling for the woman who becomes pregnant after

having a baby with NTD?

Scenario 3.         Which foods contain significant amounts of folic acid?

Scenario 4.         What percentage of folic acid is destroyed by cooking / food storage?

Scenario 5.         How many people in the UK are estimated to have a folate-deficient diet?

Scenario 6.         What is the significance of the MTHFR (Methylenetetrahydrofolate reductase gene)?

Scenario 7.         What is the significance of the Meckel-Gruber syndrome to this issue?

Scenario 8.         By what gestation has the neural tube closed?

Scenario 9.         What proportion of pregnant women have taken folic acid preconceptually?

Scenario 10.      What dose and duration of folic acid is advised for routine periconceptual use?

Scenario 11.      List the women to whom a higher dose should be offered.

Scenario 12.           How effective is periconceptual folic acid consumption in reducing NTD risk in the low-risk population?

Scenario 13.           How effective is periconceptual folic acid consumption in reducing NTD risk in women who have had an affected baby?

Scenario 14.      What is the risk of NTD recurrence for a woman who has had two affected babies?

Scenario 15.      What is the risk of NTD in Ireland?

Scenario 16.      What is the significance of the name “Bukowski” in relation to folic acid?

Scenario 17.      What effect does periconceptual folic acid have on the risk of stillbirth?

Scenario 18.           What effect does periconceptual folic acid have on the risk of autistic spectrum disorder?

Scenario 19.      What effect does periconceptual folic acid have on maternal haemoglobin levels?

Scenario 20.           What recommendations have been made by the RCOG to improve folic acid levels in pregnancy?

Scenario 21.      Which names are of importance in the history of folic acid and NTD?

Scenario 22.           What neurological condition has been thought potentially problematic with folic acid supplementation?

 

64.   Mental Capacity Act

The following scenarios relate to the Mental Capacity Act 2005. Many of the questions are not true EMQs as there is more than 1 correct answer.

Abbreviations.

COP:              Court of Protection.

FGR:              fetal growth restriction.

IMCA:           Independent Mental Capacity Advocate.

LOC:              lack of capacity.

LPA:               lasting power of attorney.

MCA:             Mental Capacity Act 2005.

PoA:              power of attorney.

Option list. Use this list unless the question has its own.

A

Yes

B

No

C

True

D

False

E

Does not exist

F

The husband

G

A parent

H

The child

I

the General Practitioner

J

the Consultant

K

the Registrar

L

The Consultant treating the patient

M

A Consultant not involved in treating the patient

N

The Medical Director

O

A person with Lasting Power of Attorney

P

The sheriff or sheriff’s deputy

Q

Balance of probabilities

R

Beyond reasonable doubt

S

None of the above.

Question 1.        Which, if any, of the following statements about the MCA are true?

A

it applies to England only

B

it applies to England & Wales only

C

it applies to England, N. Ireland, Scotland & Wales

D

it applies to adults > 18 years only

E

it applies to children 16 – 18 years

F

it applies to children < 15 years

G

it applies to men, but not to women

H

None of the above

Question 2.        Which, if any, of the following statements about the MCA are true?

A

about ½ million people fall within its remit

B

about 1 million people fall within its remit

C

about 2 million people fall within its remit

D

about 5% of acute gynaecological  admissions are of people lacking capacity at the time

E

about 10% of acute gynaecological  admissions are of people lacking capacity at the time

F

about 10% of acute medical admissions are of people lacking capacity at the time

G

about 30% of acute medical admissions are of people lacking capacity at the time

H

about 25% of psychiatric admissions are of people lacking capacity at the time

I

about 45% of psychiatric admissions are of people lacking capacity at the time

J

None of the above.

Question 3.        Which, if any, of the following terms are used in relation to the MCA Act?

A

advance decision

B

advance declaration

C

advance directive

D

advance statement

E

independent mental capacity adviser

F

lasting power of attorney

G

lingering power of attorney

H

living will

I

one-stage test of capability

J

two-stage test of capability

K

public guardian

L

temporary power of attorney

M

none of the above

Question 4.        Which of the following are legally obliged to ‘have regard’ to the MCA’s Code of

Practice in their dealings with those who lack capacity?

A

anyone involved professionally in the person’s care

B

any attorney with lasting power of attorney

C

any court-appointed deputy

D

any independent mental capacity advocate

E

anyone engaged in research involving the person lacking capacity

F

anyone paid for acts relating to the person lacking capacity

G

any care assistant involved with the person lacking capacity

Question 5.        When must the COP be involved about the implementation of  advance decisions?

Question 6.        What are the main roles of the Court of Protection?

A

to oversee implementation of MCA

B

to deal with emergency applications in relation to individuals who lack capacity

C

to appoint deputies to make decision on behalf of individuals who lack capacity

D

to appoint individuals with LPA

E

to provide legal advice to family members of someone lacking capacity

F

none of the above

Question 7.        What are the key capabilities a person must have in relation to information provided

to them to have capacity under the MCA?

A

the person must be able to read the information provided

B

the person must be able to give a clear account of the information provided

C

the person must be about to understand the information provided

D

the person must be able to retain the information provided for at least 12 hours

E

the person must be able to reach a conclusion that is logical to the doctor

F

the person must be able to communicate their decision

Question 8.        Which, if any, of the following are necessary for the appointment of someone as an

IMCA?

A

IMCA training

B

approval by the local authority

C

membership of an approved organisation

D

been cleared by the Criminal Records Bureau

E

none of the above

Question 9.        What does an IMCA do?.

Question 10.    A person with LPA is normally not a family member. True?

Question 11.    A Sheriff’s Deputy is normally not a family member. True?

Question 12.    A person with Power of Attorney can consent to treatment for the patient who lacks

capacity. True?

Question 13.    A Court-appointed Deputy can consent to treatment for the patient who lacks

capacity, but must go back to the CoP if further consent is required for additional treatment.

Question 14.    A person with PoA can authorise withdrawal of all care in cases of individuals with

persistent vegetative states.

Question 15.    An advance decision can authorise withdrawal of all but basic care in cases of

persistent vegetative states.

Question 16.    A person with PoA cannot overrule an advance direction about withdrawal or

withholding of life-sustaining care.

Question 17.    A woman is seen in the antenatal clinic at 39 weeks’ gestation. Her blood pressure is

180/110 and she has +++ of proteinuria on dipstick testing. She has mild epigastric pain. A scan shows evidence of FGR with the baby on the 2nd. centile. Doppler studies of the umbilical artery are abnormal and a non-stress CTG shows loss of variability and variable decelerations. She is advised that she appears to have severe pre-eclampsia and is at risk of eclampsia and of intracranial haemorrhage. She is told of the associated risk of mortality and morbidity. She is also advised that the baby is showing evidence of severe FGR and has abnormal Doppler studies and CTG which could lead to death or hypoxic damage. She declines admission or treatment. She says she trusts in God and wishes to leave her fate and that of her baby in His hands. She is seen by a psychiatrist who assesses her as competent under the MCA and with no evidence of mental disorder. The obstetrician wants to apply to the COP for an order for compulsory treatment. Can he do this?

Question 18.    A woman is admitted at 36 weeks’ gestation with evidence of placental abruption. She

is semi-comatose and shocked. There is active bleeding and the cervical os is closed. Fetal heart activity is present but with bradycardia and decelerations. The consultant decides that Caesarean section is the best option to save her live and that of the baby. When reading the notes, the registrar comes across an advance notice drawn up by the woman and her solicitor. It states that she does not wish Caesarean section, regardless of the risk to her and the baby. The consultant tells the registrar that they can ignore it now that she is no longer competent and get on with the Caesarean section for which she will be thankful afterwards. The registrar says that the advance notice is binding. Who is correct?

Question 19.    An 8-year-old girl is admitted with abdominal pain. Appendicitis is diagnosed with

peritonitis and surgery is advised. The parents decline treatment on religious grounds. Can the consultant in charge overrule the parents and give consent?

The TOG CPD questions for Volume 12.1 from 2010 are open access and available here.

Answer True or False.

Understanding the Mental Capacity Act 2005: a guide for clinicians

Under the Mental Capacity Act 2005:

1.     competent adults have a legal right to refuse life-threatening treatment.               True / False

2.     unwise decisions do not need to be adhered to if made by competent adults.        True / False

Advance directives:

3.     can be made by anyone aged >16 years.                                                                     True / False

4.     need only be drawn up in general terms as to a person’s wishes.                          True / False

5.     must be in writing if life-sustaining treatment is being refused.                             True / False

The following statements about advance directives are true:

6.     Refusal of basic nursing care such as oral hydration and feeding cannot be made.   True / False

7.     Oral advance decisions are never binding.                                                                  True / False

8.     Failure to recognise an advance decision may give rise to a civil wrong of trespass.              True / False

Capacity:

9.     is age related, but never task orientated.                                                                    True / False

10.   cannot be established by reference to a person’s previous behaviour or appearance.

True / False

The following statements about ‘best interests’ are true:

11.   The decision maker (doctor) is not legally obliged to consult with family members when dealing with incapacitated adults.                                                                                                 True / False

12.   Where there are disputes between the doctor and the family members regarding a patient’s best interests, getting a court appointed deputy is considered good practice.         True / False

13.   Restraint of a patient by the decision maker is allowed, as long as it is proportionate and there is a reasonable belief of harm in failing to do so.                                                          True / False

The following statements about Lasting Powers of Attorney (LPAs) are true:

14.   There are two types of LPA: one for property and affairs, the other for personal welfare.

True / False

15.   Anyone aged >16 years and with the requisite capacity is able to appoint an LPA.       True / False

16.   Where there is contradiction between a LPA and an advance directive, the latter will be the effective one.                                                                                                            True / False

Under the Mental Capacity Act 2005:

17.   patients who are only able to retain information for a short period are regarded as lacking capacity.                                                                                                                                     True / False

Which of the following statements are true?

18.   Capacity is not fixed in time and can therefore change depending on the circumstances.

True / False

19.   Parents can overrule their 16 to 17-year-old’s refusal to be admitted into a mental institution.

True / False

20    The person making an advance directive does not have to draw the attention of healthcare professionals to their decision.                                                                                      True / False

 

The TOG CPD questions for Volume 20.1 are open access and available here.

Decision-making framework in gynaecology for patients who lack mental capacity

The Mental Capacity Act of 2005:

1.     is applicable to individuals aged 18 years.                                                                 True / False

2.     is applicable to individuals residing in England and Scotland.                                  True / False

3.     is not applicable to individuals who are under the influence of drugs or substance abuse.

True / False

4.     ensures that affected individuals do not make any unwise decision with regard to their treatment.                                                                                                                  True / False

With regard to the decision-making model:

5.     substituted judgement is made to overturn an advanced decision by an individual.           True / False

6.     substituted judgement is based on the values of the concerned individual.                True / False

7.     a decision made by the method of substituted judgement is an objective means of arriving at a decision.                                                                                                                              True / False

8.     the Court of Protection is able to appoint a deputy to make a decision on behalf of a mentally incapacitated individual.                                                                                                  True / False

9.     someone with advance directive is able to demand specific life-sustaining treatment in the event of mental incapacitation.                                                                                             True / False

10.   advance statements are not valid unless they are made in writing.                       True / False

Regarding lasting power of attorney (LPA):

11.   only a person aged 18 years or more can be appointed as a donee.                     True / False

12.   a donor can appoint only one attorney with authority to make decisions.                 True / False

13.   an advance directive is still valid even when the affected person later appoints a donee with the relevant authority.                                                                                                                     True / False

14.   an individual with an LPA can decide at his or her own discretion about withdrawal of life sustaining treatment.                                                                                                   True / False

Regarding the best interests model of care:

15.   decisions made in the ‘best interests’ meeting have legal authority.                                    True / False

16.   decisions taken on this basis should be based upon personal opinion and preferences of the decision maker.                                                                                                                  True / False

17.   decisions taken on this basis should be based upon the current condition of the incapacitated person.                                                                                                                                   True / False

For assessment of mental capacity:

18.   the opinion of a psychiatrist should always be sought before a decision of mental incapacity is confirmed.                                                                                                             True / False

19.   a mini-mental state examination score of below 20 increases the likelihood of mental incapacity.                                                                                                                                True / False

Regarding the provision under the Mental Capacity Act of 2005,

20.   it allows for a decision to be taken to place a child for adoption on behalf of a mentally incapacitated person.                                                                                              True / False

 

65.   Cri du chat syndrome.

Abbreviations.

CDC:   cri du chat.

CDCs: cri du chat syndrome.

Question 1.   Which of the following are recognised alternative names for cri-du-chat syndrome?

A

5p minus syndrome

B

5p- syndrome

C

6p minus syndrome

D

6p- syndrome

E

trisomy 5

F

trisomy 6

Question 2.   Which, if any,  of the following are associated?

A

gene mutation

B

partial deletion of short arm of a chromosome

C

partial deletion of long arm of a chromosome

D

partial deletion of both arms of a chromosome

E

genetic mutation

F

translocation

G

trisomy

H

none of the above

Question 3.   Which, if any, of the following is the main cause of CDC?

A

autosomal dominant inheritance

B

autosomal recessive inheritance

C

new mutation

D

X-linked dominant inheritance

E

X-linked recessive inheritance

F

translocation

G

trisomy

H

triploidy

I

none of the above

Question 4.   What is the approximate prevalence of CDC in neonates?

A

1 in 1,000 - 5,000

B

1 in 5,000 - 10,000

C

1 in 10,000 - 20,000

D

1 in 20,000 - 50,000

E

1 in 50,000 - 100,000

F

< 1 in 1,000,000

Question 5.        Which, if any, of the following are common features of CDCs?

A

distinctive cry

B

behavioural difficulty

C

developmental delay

D

epicanthic folds

E

hypertelorism

F

hypotonia

G

leaning difficulty

H

low birthweight

I

low-set, anteriorly-rotated ears

J

microcephaly

K

small jaw

 

66.   Anatomy of the fetal skull.

Question 1.  How many bones make up the vault of the skull?

A

3

B

5

C

6

D

7

E

8

Question 2.  What is the origin of the word “bregma”?

A

the Greek word meaning “arrow”

B

the Greek word meaning “front of the head”

C

the Greek word meaning “top of the head”

D

the Greek word meaning “where lines intersect”

E

none of the above

Question 3.   What is the origin of the word “lambdoid”?

A

it is derived from “lambda”, the 11th. letter of the Greek alphabet, with the symbol “λ”

B

it is derived from the shape of the rear end of a newborn lamb, with legs apart for balance in the shape of an inverted “V”

C

it derives from the Norse noun “lam” meaning to hit

Question 4.  What is the origin of the word “sagittal”?

A

it derives from the Latin verb “sagire” meaning to be wise

B

it derives from the Latin noun “sagitta” meaning “arrow”

C

it derives from the Latin adjective “sagitta” meaning “pointing north”

D

it derives from the Latin adjective “sagitta” meaning “lacking tension”

Question 5.   What is the meaning of the word “coronal”?

A

it is the 11th. letter of the Greek alphabet

B

it derives from the Latin “corona” meaning “crown”.

C

it derives from the sun’s corona, meaning equator

Question 6.  What is the definition of “vertex”?

A

the most prominent part of the occiput

B

the area around the posterior fontanelle

C

the area bounded by the anterior fontanelle and the posterior fontanelle

D

the area bounded by the anterior & posterior fontanelles and the parietal bones

E

the area bounded by the anterior & posterior fontanelles and the parietal eminences

F

the area bounded by the anterior & posterior fontanelles and the parietal cardinals

Question 7.  What is the definition of the anterior fontanelle?

A

the anterior end of the sagittal suture

B

the area where the sagittal and coronal sutures meet

C

the area between the frontal and parietal bones

D

the posterior end of the sagittal suture

E

the area between the parietal bones and the occiput

Question 8.  What is the definition of the posterior fontanelle?

Option list. Use the option list for Question 7

Question 9.  How many other fontanelles are there?

A

0

B

2

C

3

D

4

E

6

Question 10.  What is the falx cerebri?

Option list.

A

an area of dura mater at the back of the skull like a roof over the cerebellum

B

is an artefact on ultrasound suggesting the presence of cerebral tissue where there is none

C

is the horizontal fibrous platform on which the cerebellum rests

D

is a crescent-shaped fold of dura mater separating the cerebral hemispheres

Question 11.  What is the importance of the falx cerebri in relation to delivery, particularly breech delivery?

A

the falx cerebri is inserted into the tentorium cerebelli and traction on the base of the skull may lead to tentorial tears and intracranial bleeding

B

the falx cerebri is inserted into the bone of base of the skull and traction on the base of the skull may lead to tears of the falx and intracranial bleeding

C

the falx cerebri is inserted into the tentorium cerebelli and traction on the base of the skull may lead to tentorial tears leaving the cerebellum unsupported and liable to trauma

Question 12.  What diameter presents to the pelvis with vertex presentation?

A

suboccipito-bregmatic

B

suboccipito-frontal

C

occipito-frontal

D

mento-vertical

E

submento-bregmatic

F

none of the above

Question 13.  What diameter presents to the pelvis with typical occipito-posterior position?

Option list. Use the list for Question 12.

Question14.  What diameter presents to the pelvis with brow presentation?

Option list. Use the list for Question 12.

Question 15. What diameter presents to the pelvis with mento-anterior face presentation?

Option list. Use the list for Question 12.

Question 16.  What diameter presents to the pelvis with mento-posterior face presentation?

Option list. Use the list for Question 12.

Question 17. What is the average length of the suboccipito-bregmatic diameter in a term baby?

Option list.

A

  9.0 cm.

B

  9.5 cm.

C

10.0 cm.

D

10.5 cm.

E

11.0 cm.

F

11.5 cm.

G

12.0 cm.

H

12.5 cm.

I

13.0 cm.

J

13.5 cm.

K

14.0 cm.

Question 18. What is the average length of the suboccipito-frontal diameter in a term baby?

Option list. Use the option list for Question 17.

Question 19  What is the average length of the occipito-frontal diameter in a term baby?

Option list. Use the option list for Question 17

Question 20. What is the average length of the mento-vertical diameter in a term baby?

Option list. Use the option list for Question 17

Question 21. What is the average length of the submento-bregmatic diameter in a term baby?

Option list. Use the option list for Question 17

 

67.   Flu and pregnancy.

Abbreviations.

JCVI:                 Joint Committee on Vaccination and Immunisation

MBRRACE:      MBRRACE-UK: Mothers and Babies: Reducing Risk through Audits and Confidential Enquiries across the UK.

Question 1. What did MBRRACE say about flu & pregnancy in its first report in 2014?

A

1 in 11 women died from flu

B

1 in 11 women died from flu and flu vaccination could have prevented ½ of the deaths

C

1 in 21 women died from flu

D

1 in 21 women died from flu and flu vaccination could have prevented ½ of the deaths

E

1 in 51 women died from flu

F

1 in 51 women died from flu and flu vaccination could have prevented ½ of the deaths

Question 2. How many types of flu virus are recognised?

A

3

B

5

C

10

D

15

E

>100

Question 3. Why can’t we have a universal flu vaccine?

A

The main surface antigens are haemagglutinin and neuraminidase

B

The main surface antigens are haemolysin and neuroxidase

C

The main surface antigens change frequently rendering existing vaccines impotent

D

The main core antigens change frequently, rendering existing vaccines impotent

E

The big drug companies avoid making a universal vaccine for financial reasons.

Question 4. When is flu’ most often a problem in the UK?

A

Spring

B

Summer

C

Autumn

D

Winter

E

None of the above.

Question 5. How is flu spread?

A

via aerosol or droplets from respiratory tract of an infected person

B

via aerosol or droplets from respiratory tract or direct contact with respiratory secretions  of an infected person

C

from getting drenched in cold winter showers

D

from thinking lascivious thoughts

E

from toilet seats

Question 6. What is the incubation period for flu?

A

1 – 3 days

B

1 – 7 days

C

5 – 10 days

D

up to 2 weeks

E

up to 3 weeks

Question 7. Who decides which viruses will be used in the vaccine for seasonal flu?

A

Department of Health

B

JCVI

C

the Prime Minister

D

the vaccine manufacturers

E

World Health Organisation

Question 8. How long has flu vaccination been recommended in the UK?

A

since the 1950s

B

since the 1960s

C

since the 1970s

D

since the 1980s

E

since the 1990s

Question 9. What is the recommendation about when the vaccine should be given?

A

May - July

B

June - August

C

July - September

D

August - October

E

September - November

Question 10. What advice is given about vaccination in pregnancy?

A

flu vaccine is potentially teratogenic and should be avoided before 16 weeks

B

the vaccine contains an attenuated virus with no evidence of risk in pregnancy

C

the vaccine recommended for pregnancy has no live viral material and all pregnant women are encouraged to have the seasonal vaccine

D

flu vaccine contains an attenuated virus with minimal risk, but the anti-viral drug Tamiflu is given with the vaccine to eliminate any risk of harm

Question 11. What is the H1N1 virus?

A

The avian virus which causes outbreaks of “bird flu”

B

The virus associated with “swine” flu, which caused a pandemic in 2009

C

The virus associate with MERS, currently causing deaths particularly in Saudi Arabia

D

The virus associated with simian flu

E

The virus associated with the pandemic of 1915.

Question 12. What advice should be given to pregnant women about protection against the H1N1 virus?

A

to have vaccination against H1N1 in addition to the seasonal vaccine

B

to have vaccination against H1N1 in preference to the seasonal vaccine

C

to await evidence of epidemic H1N1 flu and then have vaccination against H1N1

D

to have the seasonal vaccine as it gives good protection against H1N1

E

not to have any flu vaccination, but to take antiviral drugs if symptoms of flu occur

Question 13. Which of the following conditions have been linked to flu in pregnancy?

A

­ risk of flu complications for the mother

B

­ risk of low birthweight

C

­ risk of maternal death

D

­ risk of perinatal death

E

­ risk of  prematurity

Question 14. What is the estimated uptake of flu vaccination by pregnant women in the UK?

A

20-30%

B

30-40%

C

40-50%

D

50-60%

E

> 60%

Question 15. How many maternal deaths from flu were reported by MBRRACE for the years 2012 - 2013?

A

0

B

5

C

10

D

15

E

20

Question 16. With regard to the probable explanation for the numbers of maternal deaths from ‘flu in 2012 and 2013, which, if any, of the following statements is true?

A

the numbers reflected increased prevalence of ‘flu

B

the numbers reflected reduced prevalence of ‘flu

C

the numbers reflected improved uptake of ‘flu vaccine in pregnancy

D

the numbers reflected the introduction of Tamiflu for pregnant women with ‘flu

E

none of the above

 

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